- accession:NM_133259
- 基因别名:LRPPRC
- 基因描述:Homo sapiens leucine-rich pentatricopeptide repeat containing (LRPPRC), mRNA.
- 载体:现货载体
- CDS区长度:4185
- 翻译后氨基酸长度:1394
- 基因简介:This gene encodes a leucine-rich protein that has multiple pentatricopeptide repeats (PPR). The precise role of this protein is unknown but studies suggest it may play a role in cytoskeletal organization, vesicular transport, or in transcriptional regulation of both nuclear and mitochondrial genes. The protein localizes primarily to mitochondria and is predicted to have an N-terminal mitochondrial targeting sequence. Mutations in this gene are associated with the French-Canadian type of Leigh syndrome. [provided by RefSeq, Mar 2012]
- 规格:10ul 质粒
CDS区参考序列: 点击查看序列ATGGCAGCCCTGCTGAGATCCGCGCGTTGGTTGCTGCGTGCCGGGGCGGCCCCGCGCCTCCCGCTCTCCC
TGCGCCTCCTCCCTGGCGGCCCGGGCCGGCTGCATGCCGCCTCCTATCTGCCCGCCGCTCGCGCCGGGCC
CGTGGCCGGAGGACTACTGAGCCCAGCCAGGCTGTATGCCATTGCTGCCAAAGAAAAAGATATTCAAGAG
GAGTCCACTTTTTCTTCTAGGAAGATTTCCAATCAGTTTGATTGGGCTCTAATGAGACTAGATCTTTCTG
TTCGAAGAACTGGCCGCATTCCAAAGAAGCTTCTACAAAAAGTTTTTAATGATACCTGCCGCTCAGGTGG
CCTAGGTGGTAGTCATGCCTTGCTTCTACTACGTAGTTGTGGTTCTCTCTTGCCTGAACTAAAGCTTGAA
GAGAGAACAGAATTTGCTCATAGGATATGGGACACACTTCAGAAATTAGGTGCTGTGTATGATGTGAGTC
ACTATAATGCTTTACTTAAAGTCTATCTTCAAAATGAATATAAATTCTCACCAACTGATTTCCTGGCAAA
AATGGAGGAAGCAAACATTCAACCAAATCGAGTGACATACCAGAGATTGATTGCTTCTTATTGTAATGTA
GGAGATATTGAAGGTGCCAGCAAGATTCTTGGATTTATGAAAACTAAGGATCTCCCAGTTACAGAGGCAG
TATTCAGTGCCCTTGTGACAGGGCATGCCAGAGCTGGTGATATGGAGAATGCAGAAAACATTCTCACAGT
GATGAGAGATGCCGGAATTGAGCCTGGTCCAGACACATACCTCGCATTATTGAATGCATATGCTGAGAAG
GGCGACATTGACCATGTTAAGCAGACTCTGGAGAAGGTGGAGAAGTCCGAGCTTCACCTTATGGACCGTG
ATTTACTGCAAATTATTTTTAGCTTCAGTAAAGCTGGGTATCCTCAGTATGTCTCAGAAATTTTGGAAAA
AGTTACATGTGAAAGAAGATATATTCCAGATGCAATGAACCTCATTTTACTTTTAGTCACTGAAAAATTG
GAAGATGTAGCGTTGCAAATTTTACTAGCATGCCCCGTATCAAAGGAAGATGGCCCAAGTGTCTTTGGCA
GTTTCTTTTTACAACACTGTGTGACTATGAATACGCCTGTGGAGAAGCTAACAGACTACTGTAAGAAGTT
AAAGGAAGTCCAGATGCACTCCTTTCCTCTGCAGTTCACCCTCCATTGTGCTTTACTCGCCAATAAAACT
GATTTGGCAAAAGCCTTAATGAAGGCTGTGAAGGAGGAAGGTTTTCCTATCAGACCTCACTATTTCTGGC
CATTGCTAGTTGGACGTCGGAAGGAAAAAAATGTTCAAGGTATAATTGAAATCCTCAAAGGAATGCAAGA
ATTGGGAGTACATCCTGATCAGGAAACATATACAGATTATGTGATTCCATGCTTTGATAGTGTAAACTCA
GCACGAGCCATTTTGCAGGAAAATGGATGTCTGTCTGATAGTGATATGTTTTCTCAAGCTGGATTGAGAA
GTGAAGCAGCAAATGGGAACTTAGACTTTGTATTATCATTTTTGAAATCAAATACATTGCCCATCTCGCT
GCAGTCTATAAGAAGTAGCCTACTGCTAGGCTTCAGGAGGTCTATGAATATAAATCTTTGGAGCGAGATA
ACAGAATTGTTGTACAAGGATGGACGTTATTGCCAGGAGCCTCGAGGACCGACGGAAGCTGTTGGCTATT
TTCTTTATAACTTGATTGACAGCATGAGTGACTCAGAGGTACAGGCCAAGGAGGAGCATTTGAGACAATA
CTTCCATCAGCTGGAGAAGATGAATGTAAAAATTCCTGAAAATATCTACAGAGGCATTCGTAATCTCCTG
GAAAGCTACCATGTTCCTGAATTGATTAAGGATGCTCACTTGTTGGTTGAGAGTAAGAATTTAGACTTTC
AAAAAACTGTGCAACTTACATCATCTGAATTGGAGTCCACACTTGAAACACTAAAAGCTGAAAATCAACC
TATAAGAGATGTCCTAAAGCAACTCATATTAGTGCTTTGTTCAGAAGAGAATATGCAAAAAGCCCTTGAA
TTGAAAGCAAAATATGAATCCGACATGGTTACTGGTGGCTATGCAGCTTTAATAAATTTATGCTGTCGAC
ATGATAAAGTAGAAGATGCCTTGAACTTGAAAGAAGAATTTGACCGCTTAGATTCATCTGCTGTCCTTGA
CACCGGCAAGTATGTAGGCCTTGTAAGAGTATTGGCAAAGCATGGCAAGCTCCAAGATGCTATTAACATT
CTGAAGGAGATGAAAGAGAAGGATGTTCTTATCAAAGATACAACAGCCTTGTCCTTTTTCCACATGCTAA
ATGGCGCAGCTTTAAGAGGTGAAATTGAAACAGTAAAACAGTTGCATGAAGCCATCGTGACTCTAGGGTT
AGCAGAACCATCCACCAACATAAGTTTCCCATTGGTCACTGTACACTTGGAAAAGGGCGACCTATCTACT
GCTCTTGAGGTCGCCATTGACTGCTATGAAAAGTATAAAGTATTACCAAGGATTCATGATGTCTTGTGTA
AACTGGTAGAGAAAGGCGAGACTGATCTAATTCAGAAAGCAATGGACTTTGTGAGCCAAGAACAAGGTGA
AATGGTGATGCTCTATGATCTCTTCTTTGCCTTCCTACAAACAGGAAATTACAAAGAGGCCAAGAAGATC
ATTGAGACTCCAGGGATTAGAGCTCGATCTGCAAGGCTTCAGTGGTTTTGTGACAGATGTGTTGCAAATA
ATCAGGTTGAAACTCTGGAAAAATTAGTGGAGCTGACACAGAAGCTATTTGAATGTGATAGAGACCAGAT
GTACTACAATCTGCTAAAACTGTATAAAATAAACGGTGACTGGCAAAGAGCTGATGCAGTCTGGAATAAA
ATCCAAGAAGAAAATGTTATTCCTCGTGAAAAGACATTAAGATTATTAGCAGAAATCCTTAGAGAGGGTA
ACCAGGAAGTTCCGTTTGACGTACCTGAGTTGTGGTATGAAGATGAAAAACATTCCCTGAATTCTTCGTC
AGCCTCAACCACAGAACCTGATTTCCAGAAAGATATATTGATTGCCTGCCGATTGAACCAAAAAAAAGGG
GCATATGATATTTTCCTGAATGCAAAAGAGCAAAACATTGTGTTTAATGCTGAAACCTACAGCAATCTCA
TTAAATTACTGATGTCAGAAGATTATTTTACACAAGCAATGGAAGTGAAAGCATTCGCGGAGACCCACAT
CAAGGGCTTCACACTGAACGATGCTGCCAACAGCCGCCTCATCATAACGCAAGTTAGGCGGGATTATTTG
AAAGAGGCTGTGACAACACTGAAAACAGTATTGGATCAGCAGCAGACCCCTTCTAGGTTAGCAGTGACCC
GTGTCATCCAGGCATTGGCCATGAAGGGTGATGTTGAAAACATAGAAGTAGTTCAGAAGATGTTAAATGG
ACTCGAAGACTCCATTGGACTTTCAAAAATGGTTTTCATCAATAACATTGCTTTGGCTCAAATAAAGAAT
AATAACATAGATGCCGCAATAGAAAACATTGAAAATATGCTTACTTCAGAGAATAAAGTCATTGAACCCC
AATACTTCGGCTTGGCATACTTATTCAGAAAAGTAATAGAGGAGCAGTTGGAACCAGCAGTTGAAAAGAT
AAGCATCATGGCGGAGAGATTGGCCAATCAGTTTGCAATTTATAAACCTGTCACTGATTTTTTCCTTCAA
CTTGTGGATGCAGGCAAGGTGGATGATGCCAGAGCTCTCCTACAGAGATGTGGTGCAATTGCTGAACAAA
CCCCGATTTTGTTGTTGTTCCTCCTTAGGAATTCTAGGAAACAAGGAAAGGCATCAACTGTGAAATCTGT
GTTAGAATTGATTCCTGAATTAAATGAAAAGGAAGAAGCATACAATTCCCTCATGAAAAGCTATGTCTCA
GAGAAAGATGTCACATCTGCTAAAGCACTGTATGAACATTTGACTGCAAAGAATACAAAATTGGATGATC
TGTTTCTAAAGCGTTACGCATCTTTGCTGAAGTATGCTGGAGAGCCTGTCCCTTTCATTGAACCCCCTGA
AAGCTTTGAATTTTATGCACAGCAGCTAAGAAAATTGAGGGAAAACTCTTCTTGA翻译后氨基酸参数序列: 点击查看序列ATGGCAGCCCTGCTGAGATCCGCGCGTTGGTTGCTGCGTGCCGGGGCGGCCCCGCGCCTCCCGCTCTCCC
TGCGCCTCCTCCCTGGCGGCCCGGGCCGGCTGCATGCCGCCTCCTATCTGCCCGCCGCTCGCGCCGGGCC
CGTGGCCGGAGGACTACTGAGCCCAGCCAGGCTGTATGCCATTGCTGCCAAAGAAAAAGATATTCAAGAG
GAGTCCACTTTTTCTTCTAGGAAGATTTCCAATCAGTTTGATTGGGCTCTAATGAGACTAGATCTTTCTG
TTCGAAGAACTGGCCGCATTCCAAAGAAGCTTCTACAAAAAGTTTTTAATGATACCTGCCGCTCAGGTGG
CCTAGGTGGTAGTCATGCCTTGCTTCTACTACGTAGTTGTGGTTCTCTCTTGCCTGAACTAAAGCTTGAA
GAGAGAACAGAATTTGCTCATAGGATATGGGACACACTTCAGAAATTAGGTGCTGTGTATGATGTGAGTC
ACTATAATGCTTTACTTAAAGTCTATCTTCAAAATGAATATAAATTCTCACCAACTGATTTCCTGGCAAA
AATGGAGGAAGCAAACATTCAACCAAATCGAGTGACATACCAGAGATTGATTGCTTCTTATTGTAATGTA
GGAGATATTGAAGGTGCCAGCAAGATTCTTGGATTTATGAAAACTAAGGATCTCCCAGTTACAGAGGCAG
TATTCAGTGCCCTTGTGACAGGGCATGCCAGAGCTGGTGATATGGAGAATGCAGAAAACATTCTCACAGT
GATGAGAGATGCCGGAATTGAGCCTGGTCCAGACACATACCTCGCATTATTGAATGCATATGCTGAGAAG
GGCGACATTGACCATGTTAAGCAGACTCTGGAGAAGGTGGAGAAGTCCGAGCTTCACCTTATGGACCGTG
ATTTACTGCAAATTATTTTTAGCTTCAGTAAAGCTGGGTATCCTCAGTATGTCTCAGAAATTTTGGAAAA
AGTTACATGTGAAAGAAGATATATTCCAGATGCAATGAACCTCATTTTACTTTTAGTCACTGAAAAATTG
GAAGATGTAGCGTTGCAAATTTTACTAGCATGCCCCGTATCAAAGGAAGATGGCCCAAGTGTCTTTGGCA
GTTTCTTTTTACAACACTGTGTGACTATGAATACGCCTGTGGAGAAGCTAACAGACTACTGTAAGAAGTT
AAAGGAAGTCCAGATGCACTCCTTTCCTCTGCAGTTCACCCTCCATTGTGCTTTACTCGCCAATAAAACT
GATTTGGCAAAAGCCTTAATGAAGGCTGTGAAGGAGGAAGGTTTTCCTATCAGACCTCACTATTTCTGGC
CATTGCTAGTTGGACGTCGGAAGGAAAAAAATGTTCAAGGTATAATTGAAATCCTCAAAGGAATGCAAGA
ATTGGGAGTACATCCTGATCAGGAAACATATACAGATTATGTGATTCCATGCTTTGATAGTGTAAACTCA
GCACGAGCCATTTTGCAGGAAAATGGATGTCTGTCTGATAGTGATATGTTTTCTCAAGCTGGATTGAGAA
GTGAAGCAGCAAATGGGAACTTAGACTTTGTATTATCATTTTTGAAATCAAATACATTGCCCATCTCGCT
GCAGTCTATAAGAAGTAGCCTACTGCTAGGCTTCAGGAGGTCTATGAATATAAATCTTTGGAGCGAGATA
ACAGAATTGTTGTACAAGGATGGACGTTATTGCCAGGAGCCTCGAGGACCGACGGAAGCTGTTGGCTATT
TTCTTTATAACTTGATTGACAGCATGAGTGACTCAGAGGTACAGGCCAAGGAGGAGCATTTGAGACAATA
CTTCCATCAGCTGGAGAAGATGAATGTAAAAATTCCTGAAAATATCTACAGAGGCATTCGTAATCTCCTG
GAAAGCTACCATGTTCCTGAATTGATTAAGGATGCTCACTTGTTGGTTGAGAGTAAGAATTTAGACTTTC
AAAAAACTGTGCAACTTACATCATCTGAATTGGAGTCCACACTTGAAACACTAAAAGCTGAAAATCAACC
TATAAGAGATGTCCTAAAGCAACTCATATTAGTGCTTTGTTCAGAAGAGAATATGCAAAAAGCCCTTGAA
TTGAAAGCAAAATATGAATCCGACATGGTTACTGGTGGCTATGCAGCTTTAATAAATTTATGCTGTCGAC
ATGATAAAGTAGAAGATGCCTTGAACTTGAAAGAAGAATTTGACCGCTTAGATTCATCTGCTGTCCTTGA
CACCGGCAAGTATGTAGGCCTTGTAAGAGTATTGGCAAAGCATGGCAAGCTCCAAGATGCTATTAACATT
CTGAAGGAGATGAAAGAGAAGGATGTTCTTATCAAAGATACAACAGCCTTGTCCTTTTTCCACATGCTAA
ATGGCGCAGCTTTAAGAGGTGAAATTGAAACAGTAAAACAGTTGCATGAAGCCATCGTGACTCTAGGGTT
AGCAGAACCATCCACCAACATAAGTTTCCCATTGGTCACTGTACACTTGGAAAAGGGCGACCTATCTACT
GCTCTTGAGGTCGCCATTGACTGCTATGAAAAGTATAAAGTATTACCAAGGATTCATGATGTCTTGTGTA
AACTGGTAGAGAAAGGCGAGACTGATCTAATTCAGAAAGCAATGGACTTTGTGAGCCAAGAACAAGGTGA
AATGGTGATGCTCTATGATCTCTTCTTTGCCTTCCTACAAACAGGAAATTACAAAGAGGCCAAGAAGATC
ATTGAGACTCCAGGGATTAGAGCTCGATCTGCAAGGCTTCAGTGGTTTTGTGACAGATGTGTTGCAAATA
ATCAGGTTGAAACTCTGGAAAAATTAGTGGAGCTGACACAGAAGCTATTTGAATGTGATAGAGACCAGAT
GTACTACAATCTGCTAAAACTGTATAAAATAAACGGTGACTGGCAAAGAGCTGATGCAGTCTGGAATAAA
ATCCAAGAAGAAAATGTTATTCCTCGTGAAAAGACATTAAGATTATTAGCAGAAATCCTTAGAGAGGGTA
ACCAGGAAGTTCCGTTTGACGTACCTGAGTTGTGGTATGAAGATGAAAAACATTCCCTGAATTCTTCGTC
AGCCTCAACCACAGAACCTGATTTCCAGAAAGATATATTGATTGCCTGCCGATTGAACCAAAAAAAAGGG
GCATATGATATTTTCCTGAATGCAAAAGAGCAAAACATTGTGTTTAATGCTGAAACCTACAGCAATCTCA
TTAAATTACTGATGTCAGAAGATTATTTTACACAAGCAATGGAAGTGAAAGCATTCGCGGAGACCCACAT
CAAGGGCTTCACACTGAACGATGCTGCCAACAGCCGCCTCATCATAACGCAAGTTAGGCGGGATTATTTG
AAAGAGGCTGTGACAACACTGAAAACAGTATTGGATCAGCAGCAGACCCCTTCTAGGTTAGCAGTGACCC
GTGTCATCCAGGCATTGGCCATGAAGGGTGATGTTGAAAACATAGAAGTAGTTCAGAAGATGTTAAATGG
ACTCGAAGACTCCATTGGACTTTCAAAAATGGTTTTCATCAATAACATTGCTTTGGCTCAAATAAAGAAT
AATAACATAGATGCCGCAATAGAAAACATTGAAAATATGCTTACTTCAGAGAATAAAGTCATTGAACCCC
AATACTTCGGCTTGGCATACTTATTCAGAAAAGTAATAGAGGAGCAGTTGGAACCAGCAGTTGAAAAGAT
AAGCATCATGGCGGAGAGATTGGCCAATCAGTTTGCAATTTATAAACCTGTCACTGATTTTTTCCTTCAA
CTTGTGGATGCAGGCAAGGTGGATGATGCCAGAGCTCTCCTACAGAGATGTGGTGCAATTGCTGAACAAA
CCCCGATTTTGTTGTTGTTCCTCCTTAGGAATTCTAGGAAACAAGGAAAGGCATCAACTGTGAAATCTGT
GTTAGAATTGATTCCTGAATTAAATGAAAAGGAAGAAGCATACAATTCCCTCATGAAAAGCTATGTCTCA
GAGAAAGATGTCACATCTGCTAAAGCACTGTATGAACATTTGACTGCAAAGAATACAAAATTGGATGATC
TGTTTCTAAAGCGTTACGCATCTTTGCTGAAGTATGCTGGAGAGCCTGTCCCTTTCATTGAACCCCCTGA
AAGCTTTGAATTTTATGCACAGCAGCTAAGAAAATTGAGGGAAAACTCTTCTTGA
